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5 Facts you should know about
Progressive Familial Intrahepatic Cholestasis (PFIC)
1
Affected individuals experience severe itching, jaundice, portal hypertension, and hepatosplenomegaly
2
The hallmark feature of this disorder is severe debilitating pruritus
3
Pruritus is often out of proportion to the level of jaundice
4
Pruritus may be hard to identify in young babies because they have difficulty scratching. Instead, they may be irritable and sleep poorly
5
Scratching in babies often starts as digging at the ears and eyes, which are the first areas to show bleeding and scarring
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